Introduction: Dentigerous cyst is the most common odontogenic cyst in the jaw after radicular cyst and more frequently occurs in males at the 20s - 30s years. This cyst is commonly associated with impacted or embedded teeth, such as the third mandibular molar. Dentigerous cyst is frequently discovered accidentally when radiographs are used to investigate a failed tooth eruption or missing tooth, and it can could grow to be an ameblastoma. This case report described the diagnosis and management of a right maxillary dentigerous cyst. Case Report: A 14-year-old female visited the Oral and Maxillofacial Surgery Clinic of Cipto Mangunkusumo Hospital because she has had a swelling in her right maxilla from 3 months ago. Enucleation of the cyst along with odontectomy of the unerupted tooth were performed under general anesthesia. The diagnosis was a maxillary dentigerous cyst due to an impacted maxillary canine. Conclusion: An adequate and appropriate treatment to prevent further maxillary damage and recurrence is necessary in the rare case of maxillary dentigerous cyst. © 2020 by Nova Science Publishers, Inc. All rights reserved.